Abstract:
Aim and objectives: To review available dental literature on assessment and management of the oral manifestations of Rett syndrome.
Methodology: The Ovid Medline and Embase databases were searched for articles written in English and describing the oral manifestations of Rett syndrome and associated dental management.
Results: The search yielded 530 results in total. Ten articles focused on oral health, of which six were case reports, two case-series, one cross-sectional study, and one case-control study. Bruxism was the most frequently reported dental manifestation with dental caries less frequently reported. Management options of bite-planes, full coverage restorations and acupuncture were used for some patients.
Conclusions: Albeit with limitations, the conclusions that can be drawn are (i) The most common oral manifestation of Rett syndrome is bruxism, and more specifically, diurnal bruxism; and (ii) Although the rare incidence of Rett syndrome can be appreciated, the quality of the evidence for the management of bruxism in those with Rett syndrome subjects is poor.