The SPEC score—A quantifiable CT scoring system for primary ciliary dyskinesia

Structural lung changes seen on computed tomography scans in persons with primary ciliary dyskinesia are currently described using cystic fibrosis derived scoring systems. Recent work has shown structural changes and frequencies that are unique to PCD, indicating the need for a unique PCD-derived scoring system.

Citation:
Chowdhary T, Bracken J, Morgan L, Schultz A, Robinson P. The SPEC score—A quantifiable CT scoring system for primary ciliary dyskinesia. Pediatr Pulmonol. 2023

Keywords:
CF scoring system; CT structural changes; primary ciliary dyskinesia; spirometry

Abstract:
Structural lung changes seen on computed tomography scans in persons with primary ciliary dyskinesia are currently described using cystic fibrosis derived scoring systems. Recent work has shown structural changes and frequencies that are unique to PCD, indicating the need for a unique PCD-derived scoring system.